Sugar Tumour

A benign, circumcised but unencapsulated lung tumour characterised by exuberant vascularity, little stroma and round, polygonal glycogen-filled clear cells with well-defined borders. Sugar tumours may be surrounded by hyalinised boundaries with focal calcifications and ‘spider’ cells. They are classified as PEComas. The tumours are HMB45 +, PAS +ve and dPAS -ve