usual interstitial pneumonia


usual interstitial pneumonia

Pulmonology A condition of middle-aged individuals, often associated with connective tissue disease, characterized by insidious deterioration of respiratory function with dyspnea, tachypnea, right-sided heart failure, ↓ lung capacity, ↓ residual volume Imaging Early, 'ground-glass', linear or nodular markings, followed by coarsened shadows and cyst formation; diaphragmatic elevation in end-stage UIP reflects tissue loss Management None effective, possibly corticosteroids