释义 |
glycogenosis type 6 gly·co·ge·no·sis type 6glycogenosis due to hepatic glycogen phosphorylase deficiency, resulting in accumulation of glycogen of normal chemical structure in liver and leukocytes. Synonym(s): hepatophosphorylase deficiency glycogenosis, Hers diseasegly·co·ge·no·sis type 6 (glī'kō-jĕ-nō'sis tīp) Disorder due to hepatic glycogen phosphorylase deficiency, resulting in accumulation of glycogen of normal chemical structure in liver tissue and leukocytes. Synonym(s): Hers disease. |