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单词 gargoyle cell
释义

Gargoyle Cell

A cell, usually a histiocyte, engorged with mucopolysaccharide-laden dermatan sulfate and heparan sulfate lysosomes, seen in patients with Hurler syndrome or mucopolysaccharidosis type I-H, due to alpha-l-iduronidase deficiency
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更新时间:2025/11/22 8:31:55