CEP

porphyria

[por-fēr´e-ah] a genetic disorder characterized by a disturbance in porphyrin" >porphyrin metabolism with resultant increase in the formation and excretion of porphyrins (uroporphyrin and coproporphyrin) or their precursors; called also hematoporphyria. Porphyrins, in combination with iron, form hemes" >hemes, which in turn combine with specific proteins to form hemoproteins" >hemoproteins. hemoglobin" >hemoglobin is a hemoprotein, as are many other substances essential to normal functioning of the cells and tissues of the body.
Two general types are known: the erythropoietic porphyrias, which are concerned with the formation of erythrocytes in the bone marrow; and the hepatic porphyrias, which are responsible for liver dysfunction. Manifestations of porphyria include gastrointestinal, neurologic, and psychologic symptoms, cutaneous photosensitivity, pigmentation of the face (and later of the bones), and anemia with enlargement of the spleen. Large amounts of porphyrins are excreted in the urine and feces.
Treatment of this condition has been primarily symptomatic and varies in its effectiveness. Emphasis is on prevention of attacks by avoiding fasting and drugs that precipitate the symptoms. Photosensitivity may be controlled by avoiding exposure to light. Removal of the spleen is useful in some cases of the erythropoietic type of porphyria. Drug therapy includes the use of phenothiazines, chlorpromazine and promazine in particular. These drugs allay pain and nervousness and apparently allow a period of remission from symptoms. Meperidine hydrochloride (Demerol) may be given for pain and hydroxypheme (Hemetin) is given intravenously to compensate for genetic impairment of heme synthesis.
Patients with porphyria must not be given barbiturates, sulfonamides, alcohol, or chloroquine as these chemicals may precipitate or intensify attacks. It is recommended that persons with this disease carry with them at all times identification saying that they have porphyria so that in an emergency they will not be given medication that could precipitate an attack or even death.acute intermittent porphyria (AIP) a hereditary, autosomal dominant, form of hepatic porphyria manifested by recurrent attacks of abdominal pain, gastrointestinal dysfunction, and neurologic disturbances, and by excessive amounts of δ-aminolevulinic acid and porphobilinogen in the urine; it is due to an abnormality of pyrrole metabolism. Called also intermittent acute porphyria.congenital erythropoietic porphyria (CEP) a form of erythropoietic porphyria, with cutaneous photosensitivity leading to mutilating lesions, hemolytic anemia, splenomegaly, excessive urinary excretion of uroporphyrin and coproporphyrin, and invariably erythrodontia and hypertrichosis. Called also Günther disease.porphyria cuta´nea tar´da (PCT) the most common form of porphyria, characterized by cutaneous photosensitivity that causes scarring bullae, discoloration, growth of facial hair, and sometimes sclerodermatous thickenings and alopecia; it is frequently associated with alcohol abuse, liver disease, or hepatic siderosis. Urinary levels of uroporphyrin and coproporphyrin are increased. There are two main types: an autosomal dominant (or familial ) form in which activity of the affected enzyme is reduced to half normal in liver, erythrocytes, and fibroblasts; and a sporadic (but probably also familial) form in which the reduction is confined to the liver. Both types are believed to be heterozygous and clinical expression occurs in adulthood, precipitated by disease or environmental factors. A more severe homozygous form begins in childhood and is called hepatoerythropoietic porphyria.erythropoietic porphyria porphyria in which excessive formation of porphyrin or its precursors occurs in bone marrow erythroblasts; the group includes congenital erythropoietic porphyria and erythropoietic protoporphyria.hepatic porphyria porphyria in which the excess formation of porphyrin or its precursors is found in the liver; it includes acute intermittent porphyria, variegate porphyria, and hereditary coproporphyria.hepatoerythropoietic porphyria (HEP) a severe homozygous form of porphyria cutanea tarda believed to result from an autosomal dominant defect in the same enzyme as is affected in porphyria cutanea tarda; it is clinically identical to that disease but onset is in early childhood and enzyme activity in liver, erythrocytes, and fibroblasts is virtually absent.intermittent acute porphyria acute intermittent porphyria.porphyria variega´ta (variegate porphyria (VP)) a hereditary, autosomal dominant, type of hepatic porphyria characterized by chronic cutaneous manifestations, notably extreme mechanical fragility of the skin, particularly areas exposed to the sunlight, and by episodes of abdominal pain and neuropathy. There is typically an excess of coproporphyrin and protoporphyrin in the bile and feces.

CEP

Abbreviation for congenital erythropoietic porphyria.

CEP

Acronym	Definition
CEP➣Complex Event Processing
CEP➣Courier Express Parcel (Postal)
CEP➣Community Expansion Pack (Neverwinter Nights gaming)
CEP➣Circular Error Probable
CEP➣Centre d'Éducation Permanente (French: Center for Continuing Education; various locations)
CEP➣Campaign for an English Parliament (England)
CEP➣Consommation en Energie Primaire (French: Primary Energy Consumption)
CEP➣Christian Education Publications
CEP➣Clinical Exercise Physiologist (chronic disease assistance)
CEP➣Consejo Electoral Provisional (Spanish: Provisional Electoral Counci; Haiti)
CEP➣Center for Effective Philanthropy (Cambridge, Massachusetts)
CEP➣Common Experience Payment (Canada)
CEP➣Closer Economic Partnership (New Zealand/Thailand agreement)
CEP➣Chemical Engineering Progress (magazine)
CEP➣Cidade Estado Pais (Portuguese: City State Country)
CEP➣Character Education Partnership (Washington, DC)
CEP➣Center on Education Policy
CEP➣Community Education Partners
CEP➣Continuing Education Program
CEP➣Communications, Energy and Paperworkers Union (Canada)
CEP➣Center for Engineering and Planning (Ramallah, Palestine)
CEP➣Certified Equity Professional
CEP➣Control Engineering Practice (journal)
CEP➣Center for Emergency Preparedness
CEP➣Community Education Program (various locations)
CEP➣Configuración Energética Preestablecida (Spanish: Energy Preset Settings)
CEP➣Central Energy Plant (various locations)
CEP➣Civic Education Project
CEP➣Concurrent Enrollment Program (various schools)
CEP➣Community Engagement Program (various locations)
CEP➣Certificate Enrollment Protocol
CEP➣Clean Energy Partnership
CEP➣Circuit Establishment Packet
CEP➣Circuit Emulation over Packet
CEP➣Canon Express Protocol
CEP➣Character Education Program (advocacy group; Washington, DC)
CEP➣Center for Economic Progress (various locations)
CEP➣Committee for Environmental Protection
CEP➣Civil Emergency Planning
CEP➣Certified Estate Planner
CEP➣Cool Edit Pro (an audio program)
CEP➣Complete Environmental Products (various locations)
CEP➣Chile, Ecuador and Peru
CEP➣Civil Engineering Program (various organizations)
CEP➣Council on Epidemiology and Prevention (cardiology)
CEP➣Caspian Environment Programme
CEP➣Conferencia Episcopal Peruana (Spanish: Peruvian Episcopal Conference; Peru)
CEP➣Certificate Enrollment Protocol (Cisco/Verisign)
CEP➣Código de Endereçamento Postal (Brazilian postal code)
CEP➣Center for Environment and Population (New Canaan, Connecticut)
CEP➣Council on Economic Priorities
CEP➣Congenital Erythropoietic Porphyria
CEP➣Connecting Environmental Professionals
CEP➣Centre for European Politics (various locations)
CEP➣Civic Engagement Program (various organizations)
CEP➣Continuing Education Professional (various locations)
CEP➣Community Energy Project (various locations)
CEP➣Circulating Endothelial Precursor
CEP➣Classical Evolutionary Programming (computer programming)
CEP➣Common Entry Point
CEP➣Community Engagement Partnership (UK)
CEP➣Coastal Environment Program (Philippines)
CEP➣Custodian of Enemy Property (various locations)
CEP➣Carolina Environmental Program (University of North Carolina)
CEP➣Centre Énergétique et Procédés (French: Center for Energy and Processes; est. 1976)
CEP➣Citizenship Education Project (est. 1949)
CEP➣Contrat d'Etudes Prospectives (French: Contract for Future Studies; France)
CEP➣Centre d'Expertise de la Performance (French: Performance Expertise Center; est. 1994)
CEP➣Cell Envelope Protein (microbiology)
CEP➣Consumer Electronic Product
CEP➣Centraal Economisch Plan (Dutch)
CEP➣Continuous Evaluation Program (US Air Force)
CEP➣Conférence Européenne Permanente (French: European Standing Conference)
CEP➣Cable Entrance Panel (US DoD)
CEP➣Catalytic Extraction Processing
CEP➣Chicago Equity Partners (est 1989; Chicago, IL)
CEP➣Coordinated Examination Program
CEP➣Concurrent Enrollment Partnership (various schools)
CEP➣Centre École de Parachutisme (French skydiving school)
CEP➣Certified Environmental Professional (NAEP)
CEP➣Community Energy Programme (UK)
CEP➣Certificat d'Études Politiques (French: Certificate of Political Studies; various universities)
CEP➣Creative Economy Programme (UK)
CEP➣Certified Educational Planner
CEP➣Cyber Education Project (Philippines via satellite)
CEP➣Caribbean Environment Program
CEP➣Circle of Equal Probability (missile guidance/targeting)
CEP➣Capital Equipment Project
CEP➣Chairman's Exercise Program (US DoD)
CEP➣Celestial Ephemeris Pole
CEP➣Connection End Point
CEP➣Collège des Enseignants de Pneumologie (French: College of Teachers of Pneumology)
CEP➣Cooperative Engagement Processor
CEP➣Concept Experimentation Program
CEP➣Career Enhancement Plan
CEP➣Compensatory Education Programs
CEP➣Communications Earplug
CEP➣Centre Éducatif et Pédagogique (French: Educational and Teaching Center; Switzerland)
CEP➣Credit Enhancement Program
CEP➣Concept Evaluation Program
CEP➣Congregation for the Evangelisation of Peoples (Rome, Italy)
CEP➣Client Employed Provider
CEP➣Cooperative Enterprise Program (Cornell University; Ithaca, NY)
CEP➣College Entry Program (various schools)
CEP➣Chambre d'Économie Publique du Jura Bernois (French: Chamber of Public Economy of the Bernese Jura; Bern, Switzerland)
CEP➣Competitive Exclusion Principle
CEP➣Concept Exploration Phase
CEP➣Contact Evaluation Plot (US Navy)
CEP➣Centro de Educación para la Participación
CEP➣Centre d'Éducation Physique (French: Physical Education Center; various locations)
CEP➣Chemically Enhanced Planarization
CEP➣Combat Entry Poin (US Air Force)
CEP➣Construction Electrician (Power)
CEP➣Club Épicure Paris (French wine club)
CEP➣Certified Emergency Paramedic
CEP➣Controls for Environmental Pollution
CEP➣Central Economic Plan (The Netherlands)
CEP➣Courier-Express-Postal
CEP➣Church Extension Plan
CEP➣Condensate Extraction Pump (thermodynamics)
CEP➣Common Engine Program
CEP➣Continuing Education Project
CEP➣Conseil de l'Ethique Publicitaire (French: Advertising Ethics Council)
CEP➣Cercle des Étudiants en Philosophie (French: Undergraduate Philosophy Circle; Belgium)
CEP➣Containment Evaluation Panel
CEP➣Climatisation Électricité Plomberie (French air conditioning, electrical and plumbing company)
CEP➣Centre École Parapente (French paragliding school)
CEP➣CNO Executive Panel
CEP➣Center for Energy Policy (various locations)
CEP➣Concept Evaluation Phase
CEP➣Comptoir des Essences et Parfums (French; Tunisian perfume company)
CEP➣Contract Estimating and Pricing
CEP➣Circor Energy Products
CEP➣Computer Entry Punch
CEP➣COMSEC Equipment Program
CEP➣Cellule à Effet Peltier (French: Peltier Effect Cell)
CEP➣Cercle des Étudiants en Pharmacie (French: Pharmacy Students Circle)
CEP➣Contraintes et Preuves (French: Constraints and Proofs)
CEP➣Corridor Electro-Pneumatic (British railways vehicle)
CEP➣Civilian Employment Plan
CEP➣Combined Experiments Program
CEP➣Concept Evaluation Plan
CEP➣Credit Enhancement Provider
CEP➣Circular Error Projection
CEP➣Communications Equipment Program
CEP➣Central Engineer Park
CEP➣Commonwealth Education Project
CEP➣Curriculum Evaluation Process
CEP➣Contamination Environment Package
CEP➣Codeword Error Probability
CEP➣Circuit Emulation Protocol
CEP➣Contractor Emporium (Amperex Plant in Emporium; electronic tubes made by Amperex for US army)
CEP➣Combined Exercise Planning
CEP➣Controlled Entry Point
CEP➣Contamination Experiment Package
CEP➣Command Education Plan
CEP➣Contract Estimating & Pricing
CEP➣Containment Evaluation Priorities
CEP➣Controller Evaluation Program
CEP➣Certified Environmental Planner (American Institute of Certified Planners; American Planning Association)
CEP➣Control Electronics Package
CEP➣Congressional Engagement Plan
CEP➣C-CS Effectiveness Panel
CEP➣Culminating Experience Project
CEP➣Continuous/Continuing Evaluation Program
CEP➣Contract/or Evaluation Plan
CEP➣Cooperative Engagement Plan
CEP➣Certificate of European Pharmacopeia (certificate of suitability)

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