释义 |
branched-chain ketoaciduria
branched-chain ketoaciduria[¦brancht ¦chān ‚kēd·ō·as·ə′du̇r·ē·ə] (medicine) maple syrup urine disease branched-chain ketoaciduria
ketoaciduria [ke″to-as″ĭ-du´re-ah] the presence of ketone bodies in the urine; this condition is common in uncontrolled diabetes mellitus but can also occur anytime the body begins to break down fatty tissue to provide energy, as in starvation. Called also ketonuria.branched-chain ketoaciduria maple syrup urine disease. |