aminoadipic delta-semialdehyde synthase

a·mi·no·a·dip·ic δ-sem·i·al·de·hyde syn·thase

(ă-mē'nō-ă-dip'ik se'mē-al'di-hīd sin'thās), A bifunctional enzyme used in lysine degradation; it has a lysine:α-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinemia.