cystathionine beta-synthase


cys·ta·thi·o·nine β-syn·thase

(sis'tă-thī'ō-nēn sin'thās), An enzyme catalyzing the reversible hydrolysis of l-cystathionine to l-serine and l-homocysteine. A step in cysteine biosynthesis and in methionine catabolism. A deficiency of this enzyme leads to vascular thrombosis, dislocation of ocular lens, and abnormal development.
See also: cystathionine γ-synthase. Synonym(s): β-thionase, cysteine synthase, serine sulfhydrase