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DictionarySeeenchondromaenchondromatosis
enchondromatosis[‚en‚kän·drō·mə′tō·səs] (medicine) A rare disorder principally involving tubular bones, especially those of the feet and hands, characterized by hamartomatous proliferation of cartilage in the metaphysis, indistinguishable in single lesions from enchondromas. Also known as chondrodysplasia; dyschondroplasia; Ollier's disease. enchondromatosis
en·chon·dro·ma·to·sis (en-kon'drō-ma-tō'sis), [MIM*166000 *225795] A rare disorder characterized by hamartomatous proliferation of cartilage in the metaphyses of several bones, most commonly of the hands and feet, causing distorted growth in length and pathologic fractures; chondrosarcoma may develop. When enchondromatosis is associated with hemangiomas in the cutaneous or visceral regions, the condition is called Maffucci syndrome. Most cases are sporadic but a few instances demonstrate autosomal dominant inheritance with reduced penetrance. Synonym(s): asymmetric chondrodystrophy, dyschondroplasia, hereditary deforming chondrodystrophy (2) , Ollier diseaseen·chon·dro·ma·to·sis (en'kon-drō-mă-tō'sis) A rare familial, and probably hamartomatous, proliferation of cartilage in the metaphyses of several bones, most commonly of the hands and feet, causing distorted growth in length or pathologic fractures; chondrosarcoma frequently develops. When combined with hemangiomas in the cutaneous or visceral regions, it is called Maffucci syndrome.
Synonym(s): dyschondroplasia. Ollier, Louis Xavier Edouard Léopold, French surgeon, 1830-1900. Ollier approachOllier disease - proliferation of cartilage in the metaphyses of several bones, causing distorted growth in length or pathological fractures. Synonym(s): enchondromatosisOllier graft - a thin split-thickness graft, usually in small pieces. Synonym(s): Ollier-Thiersch graft; Thiersch graftOllier incisionOllier layerOllier methodOllier operationOllier rake retractorOllier raspatoryOllier retractorOllier techniqueOllier theory - a theory of compensatory growth.Ollier-Thiersch graft - Synonym(s): Ollier graft |