beta-hydroxypropionic aciduria

β-hy·drox·y·pro·pi·o·nic ac·i·du·ri·a

(hī-drok'sē-prō'pē-on'ik as'i-dyū'rē-ă), Elevated levels of β-hydroxypropionic acid in the urine; seen in defects in methylmalonic acid and propionate metabolism, as well as in ketotic hyperglycinemia syndrome.