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单词
purine-nucleoside phosphorylase
释义
purine-nucleoside phosphorylase
pur·ine-nu·cle·o·side phos·phor·y·lase
a ribosyltransferase that reversibly catalyzes the phosphorolysis of a purine nucleoside with orthophosphate to produce a purine and α-
d
-ribose 1-phosphate; an inherited deficiency of this enzyme leads to cellular immunodeficiency.
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