| 释义 |
pseudo-von Willebrand's disease pseudo-von Willebrand's disease Platelet-type von Willebrand disease–vWD An AD condition similar to type IIB vWD, with moderately severe Sx Lab ↑ Bleeding time, ↓ von Willebrand factor–vWF and factor VIII levels, ↑ ristocetin-induced platelet aggregation, absence of large vWF multimers and presence of the same multimers in platelets Pathogenesis Unknown; may involve platelet glycoprotein IB Management Cryoprecipitate. Cf Von Willebrand's disease. |