释义 |
phenylalanine 4-monooxygenase phen·yl·al·a·nine 4-mon·o·ox·y·gen·asean enzyme that catalyzes oxidation of l-phenylalanine to l-tyrosine with O2 and tetrahydrobiopterin (the latter forming the dihydro derivative) which is, in turn, reduced by NADPH and dihydropteridine reductase to the active form); a deficiency of either phenylalanine 4-monooxyenase or dihydropteridine reductase will result in phenylketonuria. Synonym(s): phenylalanine 4-hydroxylasephen·yl·al·a·nine 4-mon·o·ox·y·gen·ase (fen'il-al'ă-nēn mon'ō-ok'si-jĕn-ās) An enzyme that catalyzes the oxidation of l-phenylalanine to l-tyrosine; a deficiency results in phenylketonuria. Synonym(s): phenylalaninase. |