phagocytic disorder

phagocytic disorder

Phagocytic disease Immunology Any rare qualitative disorder of phagocytic WBCs, which may be familial and accompanied by generalized metabolic dysfunction; the prototypic PD is chronic granulomatous disease. See Chronic granulomatous disease. Cf Histiocytic diseases. Phagocytic Disorders Structural & functional defects Alder-Reilly anomaly • Chédiak-Higashi anomaly • Familial vacuolization of leukocytes (Jordan's anomaly) • May-Hegglin anomaly • Pelger-Huët anomaly • Pseudo- (or acquired) Pelger-Huët anomaly • Hereditary giant neutrophilia • Hereditary hypersegmentation of neutrophilic nuclei Functional defects–without structural changes • Chronic granulomatous disease • Myeloperoxidase deficiency • CD11/CD18 adhesive protein deficiency • Other enzyme defects