释义 |
DictionarySeeBecker muscular dystrophyadult pseudohypertrophic muscular dystrophy
Beck·er mus·cu·lar dys·tro·phy , Becker-type tardive muscular dystrophy (bek'ĕr), a hereditary muscle disorder of late onset, usually in the second or third decade, affecting the proximal muscles with characteristic pseudohypertrophy of the calves; clinical features similar to Duchenne muscular dystrophy but much milder and not a genetic lethal; X-linked recessive inheritance, with both Becker and Duchenne dystrophies caused by mutation in the dystrophin gene on Xp. Compare: Duchenne dystrophy. Synonym(s): adult pseudohypertrophic muscular dystrophya·dult pseu·do·hy·per·troph·ic mus·cu·lar dys·tro·phy (ă-dŭlt' sū'dō-hī'pĕr-trō'fik mŭs'kyū-lăr dis'trŏ-fē) Muscular dystrophy of late onset, often in the second or third decade, with a relatively mild course. Becker, Peter Emil, German geneticist, 1908–. Becker muscular dystrophy - a muscular dystrophy that has many of the clinical features of Duchenne muscular dystrophy. Synonym(s): adult pseudohypertrophic muscular dystrophy; Becker-type tardive muscular dystrophyBecker-type tardive muscular dystrophy - Synonym(s): Becker muscular dystrophy |