| 单词 |
methylmalonyl-coa mutase |
| 释义 |
methylmalonyl-CoA mutase
meth·yl·mal·o·nyl-CoA mu·tasean enzyme that catalyzes a reversible interconversion of l-methylmalonyl-CoA and succinyl-CoA; a cobalamin-dependent enzyme; deficiency of this enzyme will result in methylmalonic acidemia. |
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