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methylmalonyl-coa mutase
释义
methylmalonyl-CoA mutase
meth·yl·mal·o·nyl-CoA mu·tase
an enzyme that catalyzes a reversible interconversion of
l
-methylmalonyl-CoA and succinyl-CoA; a cobalamin-dependent enzyme; deficiency of this enzyme will result in methylmalonic acidemia.
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