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lipofuscinosis Translationslipofuscinosis
lipofuscinosis [lip″o-fu″sin-o´sis] any disorder due to abnormal storage of lipofuscins.neuronal ceroid-lipofuscinosis any of several genetic lipidoses characterized by progressive neurodegeneration, loss of vision, and a fatal course; included are janský-bielschowsky disease, vogt-spielmeyer disease, and kufs' disease. Formerly known as amaurotic familial idiocy.lip·o·fus·ci·no·sis (lip'ō-fyūs'i-nō'sis), Abnormal storage of any one of a group of fatty pigments; best viewed using fluorescent microscopy.lip·o·fus·ci·no·sis (lip'ō-fyūs'i-nō'sis) Abnormal storage of any one of a group of fatty pigments. lip·o·fus·ci·no·sis (lip'ō-fyūs'i-nō'sis) Abnormal storage of any one of a group of fatty pigments. |