biotinidase


bi·o·tin·i·dase

(bī'ō-tin'i-dās), An enzyme catalyzing the hydrolysis of biotin amide (forming biotin and ammonia), biocytin (forming biotin and lysine), and other biotinides. A deficiency of biotinidase can lead to organic acidemia.

biotinidase

An enzyme encoded by BTD on chromosome 3p25, which recycles biotin by cleaving biocytin (biotin-lysine), a normal product of carboxylase degradation.