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mucopolysaccharidosis vi
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mucopolysaccharidosis
mucopolysaccharidosis VI
mucopolysaccharidosis VI
Maroteaux-Lamy syndrome; MPS due to a deficiency of the enzyme
N
-acetylgalactosamine-4-sulfatase. Clinically, MPS VI is similar to MPS IH, except intelligence is normal.
See also: mucopolysaccharidosis
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