释义 |
DictionarySeeNHEncyclopediaSeeNhneonatal hemochromatosis
neonatal hemochromatosis Metabolic disease A fulminant disease characterized by massive hepatic iron loading and perinatal liver failure, accompanied by myocardial and pancreatic acinar iron overload Management Liver transplant–rarely successful. Cf Hemochromatosis, Juvenile hemochromatosis. neonatal hemochromatosis, NHA rare congenital disorder causing iron overload in the fetus and newborn, resulting in intrauterine growth retardation, premature birth, end-stage liver disease at birth, or intrauterine death. |