neonatal hemochromatosis


neonatal hemochromatosis

Metabolic disease A fulminant disease characterized by massive hepatic iron loading and perinatal liver failure, accompanied by myocardial and pancreatic acinar iron overload Management Liver transplant–rarely successful. Cf Hemochromatosis, Juvenile hemochromatosis.

neonatal hemochromatosis

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NH

A rare congenital disorder causing iron overload in the fetus and newborn, resulting in intrauterine growth retardation, premature birth, end-stage liver disease at birth, or intrauterine death.