long-chain/very long-chain acyl-CoA dehydrogenase deficiency

long-chain/very long-chain acyl-CoA dehydrogenase deficiency

a disorder of fatty acid oxidation in patients who lack the enzyme very long chain acyl-CoA dehydrogenase; sometimes manifested as weakness, hypotonia, cardiomyopathy, rhabdomyolysis, and episodes of hypoglycemia during fasting.