| 释义 |
maleylacetoacetate cis-trans-isomerase maleylacetoacetate cis-trans-isomerasean enzyme that catalyzes the reversible conversion of maleylacetoacetate to 4-fumarylacetoacetate; an enzyme that participates in l-tyrosine catabolism; a deficiency of this enzyme is associated with tyrosinemia type IB. |