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2-ketoadipic acid dehydrogenase complex
释义
2-ketoadipic acid dehydrogenase complex
2-·ke·to·a·dip·ic ac·id de·hy·dro·gen·ase com·plex
the multienzyme complex that reacts 2-ketoadipic acid with coenzyme A and NAD
+
to produce glutaryl-CoA, CO
2
, and NADH + H
+
in
l
-lysine and
l
-tryptophan catabolism; a deficiency of one of the proteins in this complex results in 2-ketoadipic acidemia.
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