(hel-weg lahr'sen), an autosomal dominant disorder characterized by anhidrotic ectodermal dysplasia and hearing loss, the latter developing in the fourth or fifth decade.
Helweg-Larssen,
Hans F., Danish dermatologist, 1917-1969. Helweg-Larssen syndrome - familial anhidrosis present from birth, with neurolabyrinthitis developing in the fourth or fifth decade.