1-phosphofructokinase

1-phos·pho·fruc·to·ki·nase

(fos'fō-frŭk'tō-kī'nās), Fructose-1-phosphate kinase; an enzyme catalyzing phosphorylation of d-fructose 1-phosphate by ATP (or other NTP) to d-fructose 1,6-bisphosphate and ADP (or other NDP); a key step in the metabolism of d-fructose; a deficiency of the muscle enzyme can result in glycogen storage disease type VII.